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Northern epilepsy (variant of neuronal corticosteroid type 8, CLN8, northern epilepsy) - rare lysosomal storage disorder of neuronal ceroidolipofuscynoz. It is caused by mutations in the CLN8 gene encoding the membrane of an endoplasmic reticulum with an unknown function. Mutations in the same genus are reported as progressive epilepsy with dementia in early postnatal period, described in children of Turkish origin; They are therefore allelic diseases. The disease is described so far in Finland only. All Finnish patients are homozygous for the Arg24Gly mutation in the CLN8 gene. The frequency of heterozygotes in the Finnish population is 1: 135. It is believed that, as with many other genetic diseases in the Finnish population, it is responsible for the effect of the founder (see Genetic Diseases in the Finnish Population). Bibliography See terms related to medical terms and related wikipedia. wiki

Masala dosa in Malaysian style Dosa (dosay in Karnataka, dosa in Andhra Pradesh, dosai தோசை in Tamil Nadu, doshai in Kerala state) - South Indian paper thin lentils made from lentil and rice flour, fried on flat plate with additive ghi. In India, the most popular version is made of fermented rice cake with added lentils, urid dal. Due to the limited availability of this variety in Europe, you can also prepare a tasty version of the whole meal. Desserts are served in many different varieties with many additions. Served with curry-seasoned vegetables they transform into masala dosa - a delicious and tasty snack. They can also be served with various chattels, such as a delicious coconut meal. Recipe Ingredients How to prepare: The dough must be smooth, which means it is smeared. Place the sieve with the smallest holes and place it in a large bowl. Add the 1 teaspoon of salt and the remaining ingredients (except oil) to the coriander leaves and finely chop. Add 2 cups of lukewar...

The process of tablet formulation in a rotary tablet press Eccentric tablet machine Rotary tablet press Tablet press - a device used to make tablets by compressing them from loose, dusty and granular materials. It is used in the pharmaceutical, chemical and food industries. There are two main types of tablets: eccentric and rotary. They differ in the mechanism that ensures the compression of the tablet with adequate force. The manufacture of tablets consists in the mechanical crushing (pressing) of granules or pellets, consisting of an active substance mixed with the appropriate excipients. Pressing is done in a suitable tablet form. There are three stages in this process: filling the matrix with the tablet, pressing and pushing the tablet out of the die opening. The main components of the tablet are: Eccentric tablet presses have a floating hopper and a fixed die. The rotary tablet press is the opposite. Pressing is done by gradually increasing the pressure of both the lower a...

Lech Tadeusz Janiszewski (born October 30, 1951 in Ostrowiec Świętokrzyski) - Polish self-government, former president of Ostrowiec Świętokrzyski and vice-governor of Świętokrzyski, member of the board of the voivodship. Curriculum vitae He graduated from the Electronics Faculty of the Wrocław University of Technology with a degree in electronics engineering. For several years he worked at Ostrowiec Hut. In the years 1990-1994 he was the president of Ostrowiec Świętokrzyski. Then up until 2000 he was employed in a joint stock company of Netia. He later worked as a director of a hospital, as well as in the Regional Development Agency and one of the municipal companies. From 2006 to 2007 he was the vice-governor of Świętokrzyskie. In the 2006 local elections, he was unsuccessful in running for the Law and Justice Sejmik. The mandate was adopted in December 2007 (in place of the elected Marek Kwitek), and was appointed as a member of the board of directors of the voivodship. In 201...

Fourth Party Logistics, 4PL (Logistic Integrator for Logistics Integrator or Lead Logistics Provider - LLP) - Virtual Suppliers with no transport means, warehouses or logistics centers in their companies. The fourth party logistics (4PL) concept was first used in 1996 by Accenture (formerly Andersen Consulting). These types of companies physically do not perform logistical processes, and their essence is to manage delivery processes by processing information. 4PL is an integrator that combines resources, capabilities, and technology from other organizations to design, build and deliver complex solutions for the entire supply chain. The system coordinates the implementation of all logistic processes that take place along the supply chain, from raw material suppliers to final buyers. The following 4PL elements are assumed: The 4PL would not be possible without the Internet and computer systems supporting the operation of the logistics at its individual stages. Bibliography ...

Patrick Lolles (born 1676, died 1739) also known as Don Patricio Laules (Lauwles) and Briaen was a Spanish diplomat. He was from a family of Irish expatriates. He participated in the Spanish Succession War (1702-1714) on the side of Filip V. From February 1713 to May 1714 was Chargé d'affaires. On his return from London, he supported the claim of Jakobick to the throne of England. In 1718 Giulio Alberoni sent him to negotiate with Swedish king Karol XII and tsar Peter I. In the years 1720-1725 Laules was a Spanish MP in Paris. Bibliography wiki

Adam ... secrets - biographical film about Adam Mickiewicz directed by Krzysztof Magowski. This film is an image of wandering in the footsteps of the poet. This journey is colored by Leszek Długosz's music and singing and the recitation of Krzysztof Kolberger. Narratorem is the author of the screenplay Krzysztof Rutkowski. The film discusses the controversial issues and unexplained situations in the biography of the poet. The authors of the picture also try to answer the question of why Mickiewicz stopped creating at some point. wiki